Results

Patients

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Fig

303 patients had dates for both symptom onset and imaging evidence of pulmonary fibrosis.

Time from symptom onset to diagnosis of IPF

Time from imaging evidence of pulmonary fibrosis to diagnosis of IPF

Characteristics at enrollment among patients with a shorter or longer time to diagnosis of IPF

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Fig

Data are % or median (Q1, Q3). GERD, gastroesophageal reflux disease. DVT, deep vein thrombosis.

Time to death or lung transplant

  • There was no significant difference in time from enrollment into the registry to death or lung transplant between patients with a longer (>1 year) versus shorter (≤1 year) time to diagnosis.

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Fig

Analyzed using a Cox proportional hazards models. 
*Adjusted model included variables previously identified as being associated with death or lung transplant in this registry (use of supplemental oxygen at rest or with activity, FVC % predicted, DLco % predicted)6 and age.

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